Prion diseases are a related group of rare, fatal brain diseases that affect animals and humans. Also known as transmissible spongiform encephalopathies (TSE), they include bovine spongiform encephalopathy ("mad cow" disease) in cattle; Creutzfeldt-Jakob disease in humans; scrapie in sheep; and chronic wasting disease in deer and elk.
Gene Name | Chromosome number | BMRB Entries | PDB Entries |
---|---|---|---|
PRNP | 20 |